MYO7A, which has purported roles in stereocilia development (Boëda et al., 2002; Prosser et al., 2008) and mechanotransduction (Li et al., 2020), has been implicated in two forms of non-syndromic deafness (DFNA11 and DFNB2; Box 1) (Liu et al., 1997; Weil et al., 1997) and in Usher syndrome (Box 1) type 1B (Weil et al., 1995). Here, MYO7A is linked to Usher syndrome.