Further, they provide a viable platform for modelling vestibular dysfunction, an often overlooked comorbidity that frequently occurs with inherited hearing loss, for example in association with mutations in CLIC5 (Seco et al., 2015), COCH (Box 1) (Robertson et al., 1998) and ESPN (Box 1) (Naz et al., 2004). The gene discussed is COCH; the disease is hearing loss disorder.