In our earlier study we presented a family with LVNC where the proband and his father, both harboring the novel MYH7 missense variant, had moderate signs of systolic dysfunction and remodeling of the left ventricle, in the absence of intramyocardial fibrosis, which allowed us to classify those patients with a relatively good prognosis [27]. The gene discussed is MYH7; the disease is left ventricular noncompaction.