The underlying pathological process is Frontotemporal Lobar Degeneration (FTLD), which can be mainly classified into two different pathological subtypes based on the typical protein aggregates present in brain tissue: the microtubule associated protein Tau (FTLD-Tau) or TAR DNA-binding protein 43 (FTLD-TDP) [2, 3]. This evidence concerns the gene MAPT and frontotemporal dementia.