Hyperparathyroidism-jaw tumor (HPT-JT) syndrome is an autosomal dominant disease that is characterized by parathyroid tumors, fibro-osseous jaw tumors of the mandible or maxilla, and renal disorders (hamartoma, cystic renal disease, or Wilms’ tumor) and results from a mutation in CDC73 (also called HRPT2) (Carpten et al., 2002). This evidence concerns the gene CDC73 and Nephroblastoma.