DSG3 and acquired polycythemia vera: Cutaneous only PV was followed in frequency in contradiction to the DCH by mucocutaneous PV in the presence of anti-Dsg3 antibodies only (22.62%), mucosal PV with anti-Dsg3-/anti-Dsg1- (17.86%), mucosal PV with anti-Dsg3+/anti-Dsg1+ (10.71%), mucocutaneous with anti- Dsg3-/anti-Dsg1- (4.76%), and equal numbers of mucocutaneous with anti-Dsg3-/anti-Dsg1+ (1.19%) or mucosal with anti-Dsg3-/anti-Dsg1+ (1.19%) (Figure 1A).