Previous research has established that the proportion of TIMM8A mutation in the population with auditory neuropathy was 1.8 %, and the deafness-myotension disorder-optic neuropathy (DDON) syndrome was caused by the unassembled DDP1/TIMM8a-TIMM13 complex in mitochondria [45]. Here, TIMM8A is linked to auditory neuropathy.