This case suggests that a similar phenotype may be manifest in Indian adolescents with JDM in association with chronic ILD.3 Mechanic’s hands are typically associated with anti-synthetase syndrome but its presence in anti-MDA5 antibody positive patients, although reported, is not well known.2,3 Thus, mechanic’s hand should also prompt testing for myositis antibodies including anti-MDA5 in Indian children with JDM. Here, IFIH1 is linked to myositis disease.