Chromosomal rearrangements that have previously been identified in SGC are MYB- or MYBL1-NFIB gene fusions in adenoid cystic carcinoma (AdCC), CRTC1- or CTRC3-MAML2 gene fusions in mucoepidermoid carcinoma (MEC), PLAG1 or HMGA2 gene fusions in carcinoma ex pleomorphic adenoma (CXPA) and ETV6-NTRK3 gene fusions in secretory carcinoma [8,9,10,11,12,13,14]. This evidence concerns the gene ETV6 and adrenocortical carcinoma, hereditary.