Multiple endocrine neoplasia type 1 (MEN1), von Hippel–Lindau disease (VHL), neurofibromatosis 1 (NF-1) (von Recklinghausen disease), and the tuberous sclerosis complex (TSC) are pancreatic endocrine tumors (PETs) [11]. Here, NF1 is linked to von Hippel-Lindau disease.