PERCC1 and hereditary disease: While historically the clinical entity of autosomal recessive congenital diarrhea in families of Iraqi-Jewish descent was designated ‘Intractable Diarrhea of Infancy Syndrome’ (IDIS), in light of our findings and in line with current shifts in the nomenclature of genetic disorders, we suggest that this entity be termed ‘PERCC1-associated congenital enteropathy’.