Neurofibromatosis type 2 (NF2) is the most common of these hereditary syndromes, but increased risk of meningioma formation also occurs in multiple endocrine neoplasia (MEN) type 1, von Hippel-Lindau (VHL), Li-Fraumeni syndrome, Gorlin syndrome, Cowden syndrome, nevoid basal cell carcinoma syndrome, BAP1 tumor predisposition syndrome, Rubinstein-Taybi Syndrome, and familial meningiomatosis (7). The gene discussed is NF2; the disease is nevoid basal cell carcinoma syndrome.