BRIP1 and Friedreich ataxia: The DNA helicase BRCA1-associated C-terminal helicase/BRCA1-interacting protein 1 (BACH1/BRIP1) is inactivated in patients with Fanconi anemia (FA); BACH1 is also known as FA complementation group (FANCJ) (Bridge et al., 2005; Levitus et al., 2005; Levran et al., 2005; Litman et al., 2005).