In addition, a n-Tr20 mutation associated with a mutation in GTP-binding protein 2 (GTPBP2)—a direct binding partner of pelota, a ribosome recycling protein—has been correlated with a significantly increased ribosome stalling at AGA codons, ataxia, and widespread neurodegeneration in the cerebellum, cortex, hippocampus, and retina areas [29]. Here, GTPBP2 is linked to cerebellar ataxia.