Examples of PPGLA mutations include the RET gene in multiple endocrine neoplasia (MEN) syndromes, the VHL gene in von Hippel–Lindau disease, the NF1 gene in Neurofibromatosis type 1, the MAX gene, or the genes of the succinate dehydrogenase complex (SDHB, SDHD, SDHA, SDHC, SDHAF2) [1,3,7,8,9]. Here, SDHD is linked to multiple endocrine neoplasia.