Patients with several congenital anomalies such as WAGR syndrome (Wilms’ tumour, aniridia, genitourinary abnormalities, intellectual disability, WT1 gene), Denys-Drash syndrome, Beckwith-Wiedermann syndrome or isolated hemihypertrophy are at higher risk of developing WT [3]. Here, WT1 is linked to Denys-Drash syndrome.