Lastly, PRNRP with a prominent tubular pattern may be confused with recently characterized low-grade oncocytic tumor or eosinophilic vacuolated tumor; however, these tumors are frequently associated with mutations involving TSC/MTOR pathways and typically lack the inverted nuclei and GATA3 positivity in PRNRP (41–43). The gene discussed is GATA3; the disease is oncocytic neoplasm.