MAPT mutations cause tauopathies that present in about 45% of cases with a bvFTD syndrome followed by unspecified dementia (34.6%), parkinsonian syndrome (4.9%), RS (4.2%), amnestic syndrome (3%), CBS (1.8%), nfaPPA (1.8%), and svPPA (1.8%) phenotypes (157). This evidence concerns the gene CBS and behavioral variant of frontotemporal dementia.