Quite often, SMARCB1-deficient sinonasal carcinoma presents as small blue round cell tumors which mimic other sinonasal malignancies including undifferentiated carcinoma, NUT sinonasal carcinoma, lymphoma, small cell carcinoma, olfactory neuroblastoma, melanoma, and rhabdomyosarcoma. The gene discussed is SMARCB1; the disease is nasal cavity and paranasal sinus carcinoma.