The provisional entities of RCC in the 2016 WHO classification include Oncocytic RCC occurring after neuroblastoma (increased risk of RCC after prior blastoma appearance similar to MiT family TRCC), thyroid-like follicular RCC (morphologically similar to the follicular carcinoma of the thyroid), Anaplastic Lymphoma Kinase (ALK) rearrangements- associated RCC (resembles medullary carcinomas and associated with sickle cell trait) and RCC with angioleiomyomatous stroma (sporadic or associated with tuberous sclerosis) (9). Here, ALK is linked to tuberous sclerosis.