There were 7 genes annotated with the term “stereocilium bundle”; USH1C, USH2A, MYO3A, TMC2, ADGRV1, PDZD7 and PKHD1L1. Most are known human deafness genes, but PKHD1L1 and TMC2 have only been identified as mouse deafness genes to date [18, 19]. This evidence concerns the gene PKHD1L1 and deafness.