Complications related to these tumours led to an NF2 diagnosis in seven patients, with headache (n = 2; median age 6.5 years [range 6–7]), cervicalgia (n = 2; median age 11.5 years [range 9–14]), brutal motor deficit (n = 1; age 9 years), intracranial hypertension (n = 1) or genito-sphincter disorders (n = 1; age 14 years). The gene discussed is NF2; the disease is intracranial hypertension.