Family with sequence similarity 107, member A (FAM107A), also known as Down-regulated in renal cell carcinoma 1 (DRR1) or Tohoku University cDNA clone A on chromosome 3 (TU3A), was firstly identified in the region of human chromosome 3p21.1, with a total length of about 10 KB and a transcript length of about 3.5 KB (10, 11). This evidence concerns the gene FAM107A and hereditary clear cell renal cell carcinoma.