†Patient died during follow-up; AMA: antimitochondrial autoantibody; AMA-M2: M2-subtype antimitochondrial autoantibodies; gp210: anti-nuclear glycoprotein 210 autoantigen; sp100: anti-nuclear sp100 autoantigen; UDCA: ursodeoxycholic acid; PBC: primary biliary cholangitis. Here, NUP210 is linked to primary biliary cholangitis.