Here we report a rare case of hereditary pheochromocytoma with a novel mutation in the succinate dehydrogenase subunit A (<i>SDHA</i>) gene.  A middle-aged woman presented with left-sided abdominal pain and was incidentally found to have bilateral adrenal lesions on abdominal imaging. The gene discussed is SDHA; the disease is hereditary pheochromocytoma-paraganglioma.