The 2022 classification criteria for MPA recently proposed by the American College of Rheumatology and the European Alliance of Associations for Rheumatology assigned the highest score of +6 to the item of “MPO-ANCA positivity” and a score of +3 to a newly added item of “fibrosis or ILD on chest imaging.” It can be said that the results of the present study are in the same context as the background in which these scores are assigned in the new criteria for MPA [15]. This evidence concerns the gene MPO and interstitial lung disease.