In C3, the 83.3% were ACs, but this also included four LCNECs, three of them harbour mutations in MEN1 and could correspond to the carcinoid-like group identified by Rekhtman et al. Median OS was not reached in C3, and was 19 and 47 months in C1 and C2, respectively. Here, MEN1 is linked to carcinoid tumor.