NF1 and neurofibromatosis type 1: Another recent cohort study showed that, among 1607 NF1 patients, 243 individuals (15.1%) developed MPNSTs, and that the 5-year disease-specific survival rate of these individuals was lower than that of patients with MPNSTs not related to NF1 (31.6% versus 43.4–71.9%) [10].