PSTPIP1 and common variable immunodeficiency: Four patients with IEI (1.01%) underwent splenectomy, 2 of whom had a diagnosis of CVID, 1 of whom had early onset multi-organ autoimmune disease, and 1 of whom had a diagnosis of proline/serine/threonine phosphatase-interacting protein 1 (PSTPIP1) deficiency.