To model the AT2 cells from DC patients, we engineered a well-characterized, causal DC mutation in DKC1 (DKC1 A386T) (Agarwal et al., 2010; Batista et al., 2011; Woo et al., 2016) into the BU3 NKX2.1::GFP SFTPC::TdTomato (NGST) human iPS cell line (Jacob et al., 2017). Here, NKX2-1 is linked to dyskeratosis congenita.