Among the miRNA-processing genes, mutations in DROSHA, DGCR8, DICER1, TARBP2, and XPO5 (encodes exportin 5) have been reported in treatment-naive and neoadjuvant chemotherapy-treated Wilms tumors (Figure 3) (121, 122, 128, 129). This evidence concerns the gene DROSHA and Nephroblastoma.