FBN1 and Weill-Marchesani syndrome: ADAMTS10 promotes fibrillin-1 microfibril assembly (Kutz et al., 2011), consistent with the observation that recessive ADAMTS10 mutations and dominantly inherited FBN1 mutations each lead to Weill-Marchesani syndrome (Dagoneau et al., 2004; Faivre et al., 2003a).