Dynein axonemal heavy chain 17 (DNAH17) is a protein of the DNAH family of which four genes have already been associated with autosomal recessive PCD, situs inversus totalis or heterotaxy, namely DNAH1, DNAH5, DNAH9, and DNAH11 [20–23]. Here, DNAH1 is linked to Situs inversus totalis.