Syndromic deafness caused by GJB2 gene mutation is often accompanied by skin diseases, including keratitis–ichthyosis–deafness (KID) syndrome [51], Bart–Pumphrey syndrome (BPS) [163], hystrix-like ichthyosis with deafness (HID) syndrome [164], and Vohwinkel syndrome [165]. This evidence concerns the gene GJB2 and KID syndrome.