However, since the beginning of the nineties of the last century, interest in the study of intermediate filaments began to actively grow since it turned out that mutations in these proteins are associated with severe skin (keratins), nervous (neurofilaments) human pathologies, including muscular dystrophies (desmin) and cardiomyopathies (desmin and vimentin) [3,4,5,6]. This evidence concerns the gene DES and cardiomyopathy.