Among them, MYO7A mutation causes nonsyndromic hearing loss DFNA11 (OMIM #601317), DFNB2 (OMIM #600060), and syndromic hearing loss Usher syndrome type 1 B (USH1B, OMIM #276900), characterized by sensorineural hearing loss, retinitis pigmentosa, and variable vestibular areflexia [3]. Here, MYO7A is linked to retinitis pigmentosa.