In a similar fashion to our results, this particular chaperone was upregulated as part of an early heat shock response in spinocerebellar ataxia‐7 (SCA7) patient‐derived fibroblasts (Scholefield et al, 2014) and in young SCA7 transgenic mouse model, while it was downregulated in older SCA7 mice (Chou et al, 2010). This evidence concerns the gene ATXN7 and spinocerebellar ataxia 7.