MUC1 and Schwartz-Jampel syndrome: Kamiya et al. studied 99 patients with SJS-ILD (with a median follow-up period of 5.97 years) and reported that a higher level of KL-6 (> 800 U/mL) was associated with poor survival (HR = 2.91, 95% CI 1.04–8.10, P = 0.04) using multivariable Cox analysis adjusted by age and gender12.