DNAJC5 and Bloom syndrome: MMP13 signal of lung sections from BLM-induced PF mice showed slightly increased than control WT mice (Figure 7B, top and middle panels), and robust increase in the signals of MMP13 were observed in ameliorated lung area in CSP-treated BLM mice that was similar to the CSP-treated Ad-TGFβ mice (Figure 7B, bottom panels: BLM + CSP).