Currently, three mouse models mimic the histopathological features of PFBC: Slc20a2 (Jensen et al., 2013) and Myorg (Yao et al., 2018) knockouts, and PDGFB hypomorph (Pdgfbret/ret, retention motif knockout) (Keller et al., 2013). This evidence concerns the gene MYORG and bilateral striopallidodentate calcinosis.