DYNC2H1 and situs inversus: Here we presented a foetus with abnormal rib curvature, narrow thorax, bilateral hypoplastic lungs, bilateral polydactyly, syndactyly and foetal visceral situs inversus with mirror-image dextrocardia presentations caused by compound heterozygous variants in DYNC2H1. These findings expanded the spectrum of DYNC2H1 variants which was more diverse and predicted important molecular functions of exon 14 of DYNC2H1. The specific sonographic findings and the molecular diagnosis helped add experience to further our expertise in prenatal counselling for SRTD3.