For an SDHA PGV carrier with an SDHA-associated tumour, with respect to the primary tumour, we would recommend at the very least annual clinical examination to include blood pressure assessment and biochemistry to include plasma metanephrines, combined with imaging of the original tumour region (eg, abdomen if phaeochromocytoma, abdominal PGL, GIST or renal tumour) if complete resection was achieved. This evidence concerns the gene SDHA and pheochromocytoma.