Previous reports have described that the presence of antineutrophil cytoplasmic antibody (ANCA) in serum was a better predictor of lung fibrosis than the presence of proteinase-3 (PR3)-ANCA was, but it did not affect the recurrence of ANCA-associated vasculitis. This was also seen in our study. The gene discussed is PRTN3; the disease is pulmonary fibrosis.