Using 3 criteria (platelets < 30 g/l, serum creatinine level < 2.273 mg/dl, and, to a lesser extent, positivity for antinuclear antibodies), it was found that the score predicts ADAMTS13 deficiency with a sensitivity of 99%, specificity of 48%, PPV of 85%, and NPV of 93%.11 This evidence concerns the gene ADAMTS13 and hyperinsulinemic hypoglycemia, familial, 4.