As it turns out, some cases initially recognized as a former Mikulicz’s disease, which is a pSS with a chronic salivary enlargement, without antibodies to ribonucleoproteins most characteristic for pSS (47)—such as anti-Sjögren’s-syndrome-related antigen A autoantibodies (anti SSA/RoAb) and anti-Sjögren’s syndrome-related antigen B antibodies (anti-SSB/La)—are now recognized as instances of IgG4-related disease (IgG4-related plasmacytic exocrinopathy) (48). Here, CALR is linked to peeling skin syndrome.