An analysis by Kölbel et al. analyzing the inflammatory infiltrates of FKRP dystroglycanopathy (LGMDR9) did not identify complement C5b-9 deposition as a component of the muscle pathology despite inflammation associated with regenerating myofibers [15]. This evidence concerns the gene FKRP and neuromuscular disease caused by qualitative or quantitative defects of alpha-dystroglycan.