COQ6 and sensorineural hearing loss disorder: For example, a 7-year-old girl from Turkey showed only SRNS without other systemic symptoms due to a homozygous COQ6 mutation c.1058C > A (p.Ala353Asp), while her elder brother harboring the same COQ6 mutation exhibited normal renal functions without any neurological presentations and developed SNHL at 10 years old (Yuruk et al., 2020).