Even though the literature describes familial forms (e.g., BRCA1-associated protein-1 (BAP1) mutation, oculodermal melanosis, familial atypical multiple mole melanoma (FAMMM) syndrome, and neurofibromatosis (NF) type I) as well as phenotypical associations, a hereditary genesis has not yet be confirmed [6,7,8]. This evidence concerns the gene BAP1 and neurofibromatosis.