MODY is a genetically heterogeneous disease and to date 14 genes (GCK, HNF1A,HNF4A, HNF1B, INS, KCNJ11, ABCC8, PDX1, NEUROD1, KLF11, CEL, PAX4, BLKand APPL1) were associated with MODY. Here, HNF4A is linked to MODY.