Certain inflammasomopathies can also present with infantile enterocolitis (71), while IEIs such as immunodysregulation polyendocrinopathy X-linked syndrome (IPEX) and X-linked inhibitor of apoptosis (XIAP) deficiency can also have similar intestinal symptoms in the neonatal period (72, 73). Here, XIAP is linked to hyperinsulinemic hypoglycemia, familial, 4.