TDP-43 pathological inclusions are seen in 97% of ALS and 45% of FTD cases, whereas FUS-positive inclusions are seen in 2% of ALS and 9% of FTD cases (Aulas and Vande Velde, 2015; Prasad et al., 2019). This evidence concerns the gene TARDBP and amyotrophic lateral sclerosis.